Fabry disease in focus

Management of Fabry disease

The information on this website is intended only to provide knowledge of Fabry disease health topics. This information should not be used in place of advice from your GP or other healthcare professional.

The Focus on Fabry website is intended for residents of the United Kingdom only. Focus on Fabry has been produced by Shire HGT, a business within the Shire group of companies. The website has been developed in accordance with industry and legal standards to provide information for the general public, patients and their families, and also healthcare professionals about Fabry disease health topics. Shire HGT makes every reasonable effort to include accurate and current information. However, the information provided on the website is not exhaustive. References for published sources of information cited on the Focus on Fabry website have been provided on the relevant pages. Please note that external links to other websites have been restricted to comply with UK pharmaceutical industry guidelines.

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Self-management

Whilst your specialist team will help with treatment, there are some things that patients and carers can do themselves to help relieve the symptoms of Fabry disease.

Diet

Gastrointestinal discomfort may be reduced if you eat small, more frequent meals. As with anyone, a healthy diet can contribute to general wellbeing, and a diet that is low in salt can help reduce the risk of heart and kidney problems.

Environment

Pain related to Fabry disease can be triggered by things such as exposure to the sun, sudden changes in temperature, physical exertion or stress. Layering clothing will enable you to adapt to changes in temperature to help keep you more comfortable, whilst drinking plenty of water before and after exercise can help relieve pain related to physical exertion. As stress is a well-documented trigger for pain and other complications, avoiding stressful or emotional situations should be a priority. This may mean planning journeys and allowing time for relaxation and regular naps.

Work

People with Fabry disease should consider an occupation that best suits their lifestyle. A career that requires a great deal of manual skill, rapid changes of temperature, physical exertion or stress should be avoided. As tiredness is a feature of Fabry disease, you should try to allow time for resting during the working day.

School

Children with Fabry disease may feel that they are different from their peers, and they may not be able to fully take part in physical activities. It is therefore useful to make teachers and school friends aware if your child has Fabry disease. There is more about this in the family life section.

General wellbeing

Illnesses can trigger pain and worsen symptoms, so regular visits to your doctor to monitor general health are an important part of overall management. As with anyone, it is advisable not to smoke or to drink alcohol in excess to help prevent damage to the heart and kidneys and reduce the risk of stroke.

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Page last updated: 10-Feb-2010